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Abstract : Restrictive cardiomyopathy (RCM) is a rare phenotype among the cardiomyopathies. It is a disorder of myocardial muscles with impaired ventricular Diastolic filling with distinct impaired hemodynamic features, raised ventricular filling pressures. The cause maybe idiopathic or secondary to systemic diseases. In countries like India the main cause for RCM is due to endomyocardial fibrosis rather than idiopathic form of RCM though the evolving pattern is now changing. We conduct a retrospective study in our Dr. D. Y. Patil Medical College among 4 patients with diagnosis of Restrictive cardiomyopathy. We analysed their demographic data, clinical manifestations, and radiographic, electrocardiographic, echocardiographic, and cardiac catheterization studies. On Echocardiography all the cases showed bi-auricular dilatation, and restrictive pattern suggestive of diastolic dysfunction. Doppler tissue imaging (TDI) shows average E/e ratio of 12 among all the 4 patients. Left ventricular systolic function was normal for all the 4 patients. Two patients underwent cardiac Catheterization, finding high RV end diastolic pressure. Cardiac MRI was performed in all the 4 patients. Four of them showed bi-auricular dilatation with preserved left ventricular systolic function & two patient had reduced right ventricular systolic function in CMR. We concluded Symptoms of heart failure such as hepatomegaly, dyspnoea, ascites is typical of Restrictive cardiomyopathy. 2D Echocardiography is the best diagnostic modality for early diagnosis and doppler tissue imaging (TDI) helps to evidence moderate to severe diastolic dysfunction. CMR can also be helpful to find the exact cause of Restrictive cardiomyopathy and obviates the need for histopathological diagnosis and biopsy.